Conservative Management of Ovarian Fibroma in A Case of Gorlin-Goltz Syndrome Comorbid with Endometriosis

Ovarian fibromas are the most common benign solid ovarian tumors, which preoperative diagnosis often is difficult. Ovarian fibromas, especially in bilateral cases, may be representative of Gorlin syndrome.Gorlin syndrome (GS) is a rare autosomal dominant disorder with predisposition to basal cell carcinomas (BCCs) and other various benign and malignant tumors. To report a case of a young patient with Gorlin syndrome and bilateral ovarian fibroma and endometriosis and septated uterus, referred to gynecology clinic of Rasoul-e-Akram hospital in October 2016. A 25years old patient with Gorlin syndrome presented with facial asymmetry, recurrent odontogenic keratocyst, multiple pigmented lesions on the trunk and face, bilateral ovarian fibroma, endometriosis and septated uterus and normal serum tumor markers. Gorlin syndrome includes numerous clinical manifestations. Diagnosis is clinical and genetic confirmation is unnecessary.In young cases of ovarian fibromas, conservative surgical management can preserve ovarian function and fertility.